Desmoplastic Fibroma of the Mandible
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چکیده
Desmoplastic fibroma of bone is a rare myofibroblastic tumor, locally aggressive, benign lesion that histologically resembles a desmoid tumor of the soft-tissue. It was initially described in 1958 by Jaffe, who separated it as a distinct entity from other intraosseous fibrous tumors. This tumor constitutes <1% of bone tumors and about 0.3% of all benign osseous tumors and it usually involves the tibia, scapula and femur [1]. The mandible represents the fourth most commonly affected site. It has a predilection to affect the posterior part of the mandible, most often in the ramusangle region. Clinical symptomatology is not specific. The imagery makes it possible to appreciate the extensive potential of the tumor .The histological appearance of the desmoplastic fibroma is identical to that of the extra-osseous desmoid, although the fibroma is infiltrative; there are no mitoses or nuclear atypia. The treatment is surgical and the quality of this treatment condition the occurrence of recurrences [1,2].
منابع مشابه
Desmoplastic fibroma of the mandible: an unusual presentation and treatment
Desmoplastic fibromas are rare, benign bone tumours, which often behave in a locally aggressive manner. In the head and neck region they are most commonly seen in the mandible and have been treated in various ways. We present an unusual presentation of the lesion, which was subsequently treated by the less commonly used technique of enucleation, with good results.
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Desmoplastic fibroma is a locally aggressive benign fibrous tumor of bone that has been reported in both the maxillofacial skeleton and the long bones. Desmoplastic fibroma of the extremities was first reported by Jaffe1 in 1958. The first description of this entity involving the jaws was reported by Griffith and Irby2 in 1965. In rare instances, multifocal desmoplastic fibromas have been repor...
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Desmoplastic fibroma (DF) is a rare, benign but locally aggressive, intraosseous lesion with a high tendency of local recurrence. In this report the actual literature is reviewed regarding epidemiological data, pathology, clinical diagnostic criterias, therapy and prognosis. Moreover, a report of an interesting case is included localized in the mandibular corpus.
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